Overview of recent advances in spinocerebellar ataxias and spastic paraplegias Masatoyo Nishizawa
1
Machado-Joseph disease/spinocerebellar ataxia type 3 Yoshihisa Takiyama
7
Spinocerebellar ataxia type 6 (SCA6) Haruo Shimazaki and Yoshihisa Takiyama
31
Spinocerebellar ataxia type 14 (SCA14) Ichiro Yabe and Hidenao Sasaki
47
Chromosome 16q22.1-linked autosomal dominant cerebellar ataxia and spinocerebellar ataxia type 4, the two clinically distinct ataxias linked to the same locus Kinya Ishikawa, Kevin Flanigan and Hidehiro Mizusawa
57
Dentatorubral-pallidoluysian atrophy (DRPLA): Clinical and genetic features, and neuroimaging Takeshi Ikeuchi, Hiroaki Nozaki and Arika Hasegawa
69
Early-onset ataxia with oculomotor apraxia and hypoalbuminemia (EAOH)/ataxia oculomotor apraxia type 1 (AOA1) Haruo Shimazaki and Yoshihisa Takiyama
81
Sacsinopathies: Sacsin-related ataxia Yoshihisa Takiyama
99
Clinical, genetic and physiopathological aspects of SPG3A/Atlastin Michito Namekawa, Alexis Brice and Merle Ruberg
113
Spastic paraplegia type 4 (SPG4) Kumi Sakoe, Michito Namekawa and Yoshihisa Takiyama
131
Polyglutamine diseases: Therapeutic strategy depends on cytotoxic structures and dysfunctions Toshiaki Takahashi, Shinichi Katada and Osamu Onodera
155
